Embryonal rhabdomyosarcoma of the biliary tree mimicking a choledochal cyst.
نویسندگان
چکیده
Embryonal rhabdomyosarcoma (ERMS) of biliary tree is a rare type of mesenchymal neoplasm diagnosed at surgery or by preoperative liver biopsy. We present a one year eight months old child who mimicked a choledochal cyst and was eventually treated with surgery, chemotherapy with IRS IV protocol and adjuvant postoperative radiotherapy to surgical bed with 6 MV photons to a dose of 5040 cGy in 28 fractions.
منابع مشابه
Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts
Jaundice in children is more often due to hepatic disease than obstruction. Differential considerations for obstructive jaundice in children include choledocholithiasis, choledochal cysts and rare neoplasms. Rhabdomyosarcoma, the most common soft tissue sarcoma in pediatric patients, typically involves the head and neck, genitourinary system and extremities. Embryonal rhabdomyosarcoma of the bi...
متن کاملRobotic-Assisted Surgery Approach in a Biliary Rhabdomyosarcoma Misdiagnosed as Choledochal Cyst
Rhabdomyosarcoma is a soft tissue malignant tumor affecting 1% of children from 0 to 14 years. Preoperative imaging may not always be diagnostic for hepatobiliary rhabdomyosarcoma and differential diagnosis with choledochal cyst (CC) could be difficult. We report a case of 2-years-old girl with a strange CC pattern of presentation. A grapelike lesion involving the choledochal and biliary ducts ...
متن کاملCholedocal Cyst in Children
During a period of two years (1984 - 1985), three patients with diagnosis of choledocal cyst have gone under operation in department of pediatric surgery (Taleghani Medical Centre). Choledochal cyst is a congenital malformation of the pancreatobiliary system. Its pathogenesis is not yet completely understood.The famale/male predisposition is 4/1. More than 50% of the patients present during the...
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Background: Hepatic tumors are rare in children comprising only 1% - 4 % of all childhood solid tumors. Primary sarcomas of the liver are extremely rare and represent approximately 0.2 % of all liver tumors. Undifferentiated embryonal sarcoma of liver is an aggressive tumor with an unfavorable prognosis. Here we reported a case of undifferentiated embryonal sarcoma of liver in a 9-year-old boy ...
متن کاملAn unusual variant of choledochal cyst: a case report
INTRODUCTION Choledochal cyst is an uncommon congenital disease of the biliary tract in the UK. There are five main types of choledochal cyst with several recognised sub-types. However, occasional variants do occur. CASE PRESENTATION We report a case of a female infant with an antenatally diagnosed choledochal cyst. The operative cholangiogram revealed an unusual intrahepatic biliary tree. Th...
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ورودعنوان ژورنال:
- Journal of cancer research and therapeutics
دوره 3 1 شماره
صفحات -
تاریخ انتشار 2007